Moya Moya disease is an idiopathic progressive occlusive cerebrovascular disorder of unknown etiology. Symptoms onset is typically in childhood or adolescence, although adult cases have been reported. Repeated ischaemic episodes are common.
Clinical course ultimately depends on the rapidity and extent of vascular occlusion and effectiveness of the collateral circulation.
Progressive stenosis or frank occlusion involving the distal ICAs and proximal aspects of the anterior and middle cerebral arteries occurs. Multiple extensive parenchymal, leptomeningeal and transdural collateral vascular channels develop.
In our case:-
Acute infarcts are seen in the distal MCA territory on the both sides. Chronic infarcts are seen in the left corona radiata.
The cervical and petrous segments of both internal carotid arteries are diffusely diminished in caliber. There is occlusion of the supraclinoid segments of both internal carotid arteries. The middle and anterior cerebral arteries are reformed by collateral circulation.
Extensive collateralisation is seen.
Imaging features are suggestive of Moya Moya disease.